Course of cystic fibrosis in black patients
| Autor: | Robert C. Stern, Carl F. Doershuk, LeRoy W. Matthews, Arthur S. Tucker, Thomas F. Boat, Frank P. Primiano |
|---|---|
| Rok vydání: | 1976 |
| Předmět: |
Male
medicine.medical_specialty Pediatrics Cystic Fibrosis Referral Black People Meconium Ileus Pulmonary disease Cystic fibrosis Pulmonary function testing Sweat gland medicine Humans Child business.industry Infant medicine.disease Respiratory Function Tests Surgery Family member medicine.anatomical_structure Respiratory failure Child Preschool Pediatrics Perinatology and Child Health Female business Follow-Up Studies |
| Zdroj: | The Journal of Pediatrics. 89:412-417 |
| ISSN: | 0022-3476 |
| DOI: | 10.1016/s0022-3476(76)80538-0 |
| Popis: | Seventeen black patients showed typical sweat gland, gastrointestinal, and pulmonary manifestations of cystic fibrosis. There was an unusually high incidence of meconium ileus equivalent (35%). Three infant siblings of patients in this study had died of cystic fibrosis prior to referral of a family member to this center. One patient died at age four years after emotional problems interfered with the treatment program; status asthmaticus played a major role in his terminal respiratory failure. The remainder of the patients have had substantially less morbidity from pulmonary disease than a comparable, much larger group of white patients. Only one patient, age 28, who is married and employed full-time has severe pulmonary involvement as assessed by pulmonary function studies and chest roentgenogram. The 16 surviving patients have a mean age of 13 1/2 years after a mean follow-up period of 10 years. If black patients with cystic fibrosis survive infancy, they then, as a group, may have a relatively good prognosis. |
| Databáze: | OpenAIRE |
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