Sarcoidosis-induced pericarditis in a patient with portopulmonary hypertension: a case report
| Autor: | Alexander Mpoumponaris, Kalliopi Patsiaoura, Nikolaos Eugenidis, Olga Giouleme, Panagiotis Anagnostis, Nikolaos Grammatikos, Elias Basayannis, Nikitas Kakavas, Themistoklis Vasiliadis |
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| Jazyk: | angličtina |
| Rok vydání: | 2009 |
| Předmět: |
Medicine(all)
medicine.medical_specialty Portopulmonary hypertension Pathology Cirrhosis business.industry Pericardial fluid General Medicine medicine.disease Pulmonary hypertension Bosentan Pericarditis Acute pericarditis Internal medicine Case report medicine Cardiology Portal hypertension business medicine.drug |
| Zdroj: | Cases Journal |
| ISSN: | 1757-1626 |
| Popis: | Portopulmonary hypertension is a rare and severe complication of patients with cirrhosis. Sarcoidosis, a disease of unknown etiology, is also a cause of pulonary hypertension and right heart dysfunction. We report the case of a 51-year-old male patient, suffering from cirrhosis due to Wilson's disease, portal hypertension and pulmonary hypertension (PH), who developed severe pericarditis. Wilson's disease was diagnosed 8 years before his last admission to our hospital and was being successfully treated with D-penicillamine. PH was recognized 2 years before admission and being treated with bosentan. The patient complained for dyspnea at rest and the 2D echocardiogram revealed a significant amount of pericardial fluid. All other causes of acute pericarditis were excluded and his laboratory, imaging and histopathological investigation showed evidence of sarcoidosis. He underwent a therapy with corticosteroids (methylprednisolone) and his follow-up examination showed remarkable decrease of the levels of mean pulmonary artery pressure and pericardial fluid. |
| Databáze: | OpenAIRE |
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