Dowling-Degos Disease Presenting With Associated Epidermal Inclusion Cysts: A Case Report and Review of the Literature
| Autor: | Mark S. Lincoln, Lisa M. Marinelli, Kathleen C. Marinelli, Amanda M. Roberts |
|---|---|
| Rok vydání: | 2021 |
| Předmět: |
Adult
Male medicine.medical_specialty Dowling-Degos Disease business.industry Skin Diseases Papulosquamous Epidermal Cyst Genodermatosis Skin Diseases Genetic Dermatology General Medicine Disease Intertriginous equipment and supplies medicine.disease Hyperpigmented macules Pathology and Forensic Medicine Hyperpigmentation Dermatologic diseases Medicine Humans Hidradenitis suppurativa business Progressive disease |
| Zdroj: | The American Journal of dermatopathology. 44(3) |
| ISSN: | 1533-0311 |
| Popis: | Dowling-Degos Disease (DDD) is a rare and disfiguring autosomal dominant genodermatosis characterized by reticulate hyperpigmented macules or follicular comedone-like papules in the intertriginous areas that typically presents in the third or fourth decade of life. It is a progressive disease that is often treatment-resistant. Although its association with hidradenitis suppurativa has been well described, DDD has also been less commonly reported in conjunction with other dermatologic diseases with unknown etiologic associations. Herein, we present a case of DDD with associated epidermal inclusion cysts and conduct a literature review of dermatologic conditions reported in association with DDD. |
| Databáze: | OpenAIRE |
| Externí odkaz: |
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