Primary ectopic frontotemporal craniopharyngioma
| Autor: | Juan Luis Gómez-Amador, Juan Antonio Ponce-Gomez, Martha Lilia Tena-Suck, Luis Alberto Ortega-Porcayo, Mauricio Martínez-Moreno, Lesly Portocarrero-Ortiz |
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| Jazyk: | angličtina |
| Předmět: |
Pathology
medicine.medical_specialty Suprasellar region medicine.diagnostic_test business.industry Craniopharyngeal duct Case Report Computed tomography Karnofsky Performance Status Scale medicine.disease CSF cerebrospinal fluid Craniopharyngioma Ectopic Keyhole CT computed tomography Metaplastic Change Endoscopic KPS karnofsky performance status scale medicine Surgery business MRI magnetic resonance imaging |
| Zdroj: | International Journal of Surgery Case Reports |
| ISSN: | 2210-2612 |
| DOI: | 10.1016/j.ijscr.2014.12.038 |
| Popis: | Highlights • We described the first case of a primary ectopic fronto-temporal craniopharyngioma. • A primary ectopic craniopharyngioma is a tumor that arises for the first time without previous surgery in any compartment with no midline involvement from remnants of the Rathke’s pouch. • Keyhole endoscopic approach gives a better screen image of neurovascular elements, better illumination and less brain retraction. Introduction Primary ectopic craniopharyngiomas have only rarely been reported. Craniopharyngiomas involve usually the sellar and suprasellar region, but can be originated from cell remnants of the obliterated craniopharyngeal duct or metaplastic change of andenohypophyseal cells. We present the first case of a primary ectopic frontotemporal craniopharyngioma. Presentation of case A 35-year old woman presented with a one-year history of headache and diplopia. MRI showed a large frontotemporal cystic lesion. Tumor resection was performed with a keyhole endoscopic frontal lateral approach. The pathological features showed an adamantinomatous craniopharyngioma with a cholesterol granuloma reaction. Discussion There have been reported different localizations for primary ectopic craniopharyngioma. Our case presented a lobulated frontotemporal cystic mass formed by a dense eosinophilic proteinaceous material dystrophic calcifications and cholesterol crystals, with epithelial remnants. No tumor regrowth was observed in the magnetic resonance image 27 months postoperatively. Conclusion Primary ectopic craniopharyngioma is a rare entity with a pathogenesis that remains uncertain. This is an unusual anatomic location associated with unique clinical findings. |
| Databáze: | OpenAIRE |
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