Miyazaki syndrome: Cervical myelo/radiculopathy caused by overshunting. A systematic review
Autor: | Anna Szűcs, Balázs Markia, Dusan Vitanovics, Zoltan K. Nagy, Gábor Nagy, Eva Osztie, Péter Várallyay, János Vajda, Gábor Czigléczki |
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Rok vydání: | 2019 |
Předmět: |
Adult
Male medicine.medical_specialty Nerve root Adolescent Intracranial Hypotension Ventriculoperitoneal Shunt Spinal Cord Diseases 03 medical and health sciences Myelopathy 0302 clinical medicine Cerebrospinal fluid medicine Humans Radiculopathy business.industry Venous plexus General Medicine Syndrome medicine.disease Spinal cord Pathophysiology Surgery Shunt (medical) Prosthesis Failure Shunting medicine.anatomical_structure 030220 oncology & carcinogenesis Cervical Vertebrae Female Neurology (clinical) business 030217 neurology & neurosurgery |
Zdroj: | Clinical neurology and neurosurgery. 186 |
ISSN: | 1872-6968 |
Popis: | Objectives Miyazaki syndrome is a cervical myelopathy or radiculopathy caused by cervical epidural venous congestion, due to cerebrospinal fluid over-drainage by an implanted ventricular shunt. The complex pathophysiology includes CSF pressure-changes consistent with the Monro-Kellie doctrine and a non-functional Starling resistor, leading to spinal epidural venous plexus enlargement and dilation. This venous congestion may be significant enough to exert compression on the spinal cord or nerve roots. The typical clinical and imaging findings together with a history of ventricular CSF shunting may establish the diagnosis, proven by a successful treatment. The aim of treatment is the abrogation of CSF over-drainage. The eligible interventions may be the followings: the increase of the opening-pressure of the valve system by the insertion of a new programmable valve if necessary, closing or removing the shunt. Aim We want to call attention to this rare iatrogenic condition with potentially severe consequences. Patients and Methods We perform a systematic literature-review and present our five cases. Results Once recognized in time, Miyazaki syndrome can be well taken care of. Conclusions Patients with chronic ventricular shunt need monitoring for CSF over-drainage to recognise potential complications such as cervical myelopathy or radiculopathy. |
Databáze: | OpenAIRE |
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