Bernard-Soulier syndrome in pregnancy
| Autor: | L. A. Parapia, P. Prabu |
|---|---|
| Rok vydání: | 2006 |
| Předmět: |
Adult
Blood Platelets Erythrocyte transfusion medicine.medical_specialty Adolescent Platelet Aggregation Platelet disorder Clinical Biochemistry Platelet Transfusion Consanguinity Bernard–Soulier syndrome Pregnancy hemic and lymphatic diseases medicine Humans Deamino Arginine Vasopressin In patient business.industry Obstetrics Postpartum Hemorrhage Pregnancy Complications Hematologic Biochemistry (medical) Bernard-Soulier Syndrome Hematology General Medicine medicine.disease Postpartum haemorrhage Platelet transfusion Tranexamic Acid Female sense organs Erythrocyte Transfusion business |
| Zdroj: | Clinical and Laboratory Haematology. 28:198-201 |
| ISSN: | 1365-2257 0141-9854 |
| DOI: | 10.1111/j.1365-2257.2006.00780.x |
| Popis: | Bernard-Soulier syndrome (BSS) is a rare autosomal recessively inherited bleeding disorder. Pregnancy in patients with BSS is characterized by ante-, intra-, or postpartum haemorrhage, which may be delayed and severe. There is no consensus in the management of BSS in pregnancy and so far only 16 pregnancies in nine patients have been described. We report a further three pregnancies in two women with the syndrome. We also outline our management of pregnant patients with BSS. |
| Databáze: | OpenAIRE |
| Externí odkaz: |
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