Primary leiomyosarcoma of the great saphenous vein: A case report
| Autor: | Norberto J. Torres-Lugo, Ruben Tresgallo-Parés, Lucas G. De Virgilio-Salgado, Natalia A. Asenjo-Molina, Norman Ramirez, Juan Bibiloni-Rodríguez |
|---|---|
| Rok vydání: | 2021 |
| Předmět: |
Leiomyosarcoma
medicine.medical_specialty SMA Smooth Muscle Actin medicine.medical_treatment Case Report GSV Great Saphenous Vein Excision Asymptomatic Inferior vena cava CD-US Color Doppler Ultrasound MRI Magnetic Resonance Imaging Metastasis Recurrence Medicine IVC Inferior Vena Cava SMS Smooth Muscle Sarcoma business.industry Great saphenous vein VL Vascular Leiomyosarcoma CT Computed Tomography medicine.disease Radiation therapy medicine.vein Primary Leiomyosarcoma Surgery Radiology Sarcoma medicine.symptom business |
| Zdroj: | International Journal of Surgery Case Reports |
| ISSN: | 2210-2612 |
| DOI: | 10.1016/j.ijscr.2021.106565 |
| Popis: | Introduction and importance Vascular smooth muscle sarcomas are rare neoplasms that comprise less than 2% of all leiomyosarcomas. These malignancies usually originate in the inferior vena cava, with a limited number of cases affecting the great saphenous vein. Due to the limited reports on these sarcomas, epidemiologic data remains insufficient. Case presentation We report the case of a 67-year-old Hispanic female that presented with an asymptomatic growing mass in her right thigh. She was managed with an En bloc resection under the impression of a smooth muscle vascular sarcoma. The diagnosis was confirmed after histopathologic evaluation. Clinical discussion Vascular leiomyosarcomas remain a rare and challenging diagnosis. They usually present as a slowly growing mass that is initially asymptomatic. High clinical suspicion and a comprehensive radiologic evaluation, including magnetic resonance imaging, are crucial. Histopathological evaluation is essential for diagnostic confirmation. Surgical excision remains the treatment of choice, with radiation therapy mostly considered for local disease control. Postsurgical surveillance is necessary every three months to monitor for signs of recurrence. Conclusion Physicians should remain aware of the nonspecific presentation of leiomyosarcomas and the importance of a comprehensive diagnostic approach. Early diagnosis and adequate management are fundamental elements in the treatment of these aggressive tumors. Highlights • Consider leiomyosarcoma within the differential diagnosis of a painless enlarging mass. • Doppler ultrasound and magnetic resonance imaging are valuable diagnostic tools. • Data support radiation therapy for local control of these neoplasms. • This case contributes to the limited literature regarding the epidemiology and treatment of these tumors. |
| Databáze: | OpenAIRE |
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