Scimitar syndrome with absent right pulmonary artery and severe pulmonary hypertension treated with coil occlusion of aortopulmonary collaterals in a term neonate
| Autor: | Husam Salama, Hussain Parappil, Faraz Masud, Sajjad Rahman |
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| Rok vydání: | 2015 |
| Předmět: |
Male
medicine.medical_specialty Cardiac Catheterization Hypertension Pulmonary Collateral Circulation Pulmonary Artery Coronary Angiography Article Pulmonary hypoplasia Scimitar syndrome Furosemide Internal medicine medicine Humans Diuretics Heart Failure Respiratory Distress Syndrome Newborn Respiratory distress business.industry Vascular disease Scimitar Syndrome Infant Newborn General Medicine medicine.disease Right pulmonary artery Pulmonary hypertension Surgery Treatment Outcome Respiratory failure Echocardiography Cardiology cardiovascular system business Rare disease |
| Zdroj: | BMJ case reports. 2015 |
| ISSN: | 1757-790X |
| Popis: | Scimitar syndrome (SS) is a rare congenital malformation with an estimated incidence of approximately 2 in 100 000 births. A wide clinical spectrum is observed in children with this syndrome. The common clinical presentation in infancy is respiratory distress and tachypnoea due to associated pulmonary hypoplasia, pulmonary overcirculation and/or pulmonary hypertension. Babies with SS presenting with cardiac failure are prone to develop exaggerated pulmonary vascular disease. Hence early intervention, using either coil embolisation or surgical intervention, is indicated. We are reporting a case of a term baby boy who presented with respiratory failure during the first 24 h of life. Echocardiogram and CT angiogram revealed SS. The baby needed intubation due to respiratory failure. Aortopulmonary collaterals, identified on aortic angiogram, were successfully occluded with detachable coils. |
| Databáze: | OpenAIRE |
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