Successful Repair of Infantile Scimitar Syndrome with Contralateral Pulmonary Vein Stenosis in an Infant
| Autor: | Mehmet Akif Önalan, Selim Aydin, Ersin Erek, Bahar Temur |
|---|---|
| Přispěvatelé: | Acibadem University Dspace |
| Rok vydání: | 2021 |
| Předmět: |
Heart Defects
Congenital medicine.medical_specialty RD1-811 Heart disease Case Report Constriction Pathologic 030204 cardiovascular system & hematology Congenital 03 medical and health sciences 0302 clinical medicine Scimitar syndrome Diseases of the circulatory (Cardiovascular) system Medicine Humans Survivors Pulmonary vein stenosis Pulmonary Syndrome Heart Defects Surgical approach business.industry High mortality Scimitar Syndrome Infant General Medicine medicine.disease Surgery Stenosis Pulmonary Vein Pulmonary Veins RC666-701 Respiratory System Abnormalities Cardiology and Cardiovascular Medicine business Hypoplastic lung |
| Zdroj: | Brazilian Journal of Cardiovascular Surgery Brazilian Journal of Cardiovascular Surgery, Vol 36, Iss 1, Pp 133-136 (2020) |
| ISSN: | 1678-9741 |
| Popis: | Infantile scimitar syndrome (SS) is a rare congenital heart disease and has high mortality. Guidelines have not been established, but surgery is indicated in symptomatic patients. Despite the various surgical approaches, outcomes continue to be disappointing. We present our surgical experience with an infantile SS patient who had stenotic pulmonary veins contralateral to the hypoplastic lung with complicated anatomy. There are few cases with this complex pathology in the literature. Moreover, our patient was the first transplant-free survivor with this complexity in the literature. |
| Databáze: | OpenAIRE |
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