Recurrent hepatobiliary sepsis in a patient with von Meyenburg complexes: a case report and review of the literature
| Autor: | Wei Qiang Leow, Gabrielle Slapak, Doreen Siew Ching Koay, Thuan Tong Tan |
|---|---|
| Jazyk: | angličtina |
| Rok vydání: | 2017 |
| Předmět: |
Pediatrics
medicine.medical_specialty medicine.drug_class business.industry medicine.medical_treatment Antibiotics lcsh:R lcsh:Medicine General Medicine Liver transplantation medicine.disease Asymptomatic Sepsis 03 medical and health sciences 0302 clinical medicine 030220 oncology & carcinogenesis medicine 030211 gastroenterology & hepatology Presentation (obstetrics) medicine.symptom Intensive care medicine business Medical therapy Immunodeficiency Von Meyenburg complexes |
| Zdroj: | Proceedings of Singapore Healthcare, Vol 26 (2017) |
| ISSN: | 2059-2329 2010-1058 |
| Popis: | The von Meyenburg complex (VMC) is a rare, congenital malformation of the ductal plate. It is typically asymptomatic and usually discovered incidentally. We report a unique case of recurrent life-threatening hepatobiliary sepsis caused by VMC and a review of the literature. A 62-year-old man presented with recurrent episodes of life-threatening hepatobiliary sepsis. Extensive investigations only showed that he has VMCs without any other source of sepsis or underlying immunodeficiency states. Despite prolonged courses of antibiotics which resolved each episode of sepsis, he suffers repeated recurrences of hepatobiliary sepsis. Liver transplantation is now being considered in view of his refractoriness to medical therapy. As VMC can present with severe hepatobiliary sepsis, it is therefore essential to recognise its presence. This case adds to the literature the atypical but life-threatening clinical presentation of VMC. |
| Databáze: | OpenAIRE |
| Externí odkaz: |
|