The Key Search Subtest of the Behavioural Assessment of the Dysexecutive Syndrome in Children (BADS-C) Instrument Reveals Impaired Planning Without External Constraints in Children With Neurofibromatosis Type 1
| Autor: | Roberto Micheli, Veronica Saletti, Daria Riva, Chiara Vago, Sara Bulgheroni, Silvia Esposito, Alessandra Erbetta |
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| Rok vydání: | 2017 |
| Předmět: |
Male
Neurofibromatosis 1 Adolescent Neuropsychological Tests 050105 experimental psychology Task (project management) Developmental psychology Thinking 03 medical and health sciences Executive Function 0302 clinical medicine medicine Humans 0501 psychology and cognitive sciences Prospective Studies Neurofibromatosis Child Dysexecutive syndrome Analysis of Variance Siblings 05 social sciences Case-control study Wechsler Scales Wechsler Adult Intelligence Scale Brain Executive functions medicine.disease Magnetic Resonance Imaging Hyperintensity Case-Control Studies Pediatrics Perinatology and Child Health Key (cryptography) Female Neurology (clinical) Psychology 030217 neurology & neurosurgery Clinical psychology |
| Zdroj: | Journal of child neurology. 32(4) |
| ISSN: | 1708-8283 |
| Popis: | Studies of executive function and its relationship with brain T2-weighted hyperintensities in children with neurofibromatosis type 1 (NF1) have yielded inconsistent results. We examined 16 children with NF1 aged 8 to 15 years, of normal intelligence, and compared their findings to those of 16 siblings and 16 typically developing children using the Behavioural Assessment of the Dysexecutive Syndrome in Children (BADS-C). NF1 patients had an adequate overall score at BADS-C, but showed significantly lower performance than typical peers in the Key Search subtest. This is a task that must be solved without any given rules, in which subjects must devise a strategy and an efficient search pattern transferable to other similar real situations. The Key Search scores were not correlated with number and signal characteristics of T2-weighted hyperintensities. Planning without external indications is impaired in children with NF1 because they have to rely entirely on self-organization and monitoring; this study provides information for remediation programs designed to improve functioning in daily life. |
| Databáze: | OpenAIRE |
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