Melanotic neuroectodermal tumor of infancy (MNTI) of the hard palate: presentation and management

Autor: Robert B. McLaughlin, David F. Carpentieri, Udayan K. Shah, Robert Puchalski, Steven D. Handler
Rok vydání: 2000
Předmět:
Zdroj: International Journal of Pediatric Otorhinolaryngology. 53:163-168
ISSN: 0165-5876
DOI: 10.1016/s0165-5876(00)00315-3
Popis: Objective: To discuss the presentation and management of melanotic neuroectodermal tumor of infancy (MNTI) of the hard palate. Method: Case presentation and literature review. Case : A 6-month-old girl presented with a slow growing, non-tender anterior oral hard palate mass. Radiologic imaging revealed a well-circumscribed cystic lesion containing teeth. After excision, histopathologic and electron microscopic evaluation revealed MNTI. No recurrence was seen at 12-month follow-up. Conclusions: This case and a review of the literature reveal MNTI to be a rare, benign hard palate tumor, which may present as a smooth, firm, painless, slow-growing anterior palatal lesion. Imaging reveals a well-circumscribed cystic lesion. Complete excision should be curative. Management requires attention to the potential need for palatal reconstruction, orthodontic care and correction of secondary nasal deformities.
Databáze: OpenAIRE