Oncocytic Papillary Renal Cell Carcinoma in an 11-year-old girl
| Autor: | Haydar Asad, Jabbour Teddy, Ghandour Fatme, Akl Bernard, Bedoyan Zarouhie, Jabbour Michel |
|---|---|
| Rok vydání: | 2021 |
| Předmět: |
Pathology
medicine.medical_specialty Urology media_common.quotation_subject medicine.medical_treatment 030232 urology & nephrology Disease 03 medical and health sciences 0302 clinical medicine Renal cell carcinoma Rare case Medicine Humans Girl Child Carcinoma Renal Cell media_common Genetic testing Papillary renal cell carcinomas medicine.diagnostic_test business.industry medicine.disease Nephrectomy Kidney Neoplasms 030220 oncology & carcinogenesis Female business Renal carcinoma |
| Zdroj: | Urology. 156 |
| ISSN: | 1527-9995 |
| Popis: | Oncocytic Papillary Renal Cell Carcinoma (OPRCC) is a rare variant of renal cell carcinoma with overlapping characteristics type 1 and 2 of papillary renal carcinoma. Based on the literature, OPRCC is predominantly present in adult males. OPRCC has a specific genetic affiliation with the Fumarate Hydratase gene requiring all patients diagnosed with OPRCC to undergo genetic testing. There isn't any agreement for the treatment of OPRCC due to the rarity of the disease; however, a radical nephrectomy poses as a possible modality. Therefore, we present the rare case of an 11-year-old female found to have OPRCC. |
| Databáze: | OpenAIRE |
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