Familial Henoch-Schönlein Syndrome
| Autor: | Gregorio P. Milani, Alessandra Ferrarini, Giorgia Pellanda, Mario G. Bianchetti, Giacomo D. Simonetti, Alessandro Ostini |
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| Rok vydání: | 2016 |
| Předmět: |
Adult
Male Pediatrics medicine.medical_specialty Adolescent IgA Vasculitis Nephropathy 03 medical and health sciences Young Adult 0302 clinical medicine Age Distribution Rheumatology immune system diseases hemic and lymphatic diseases medicine Humans 030212 general & internal medicine Young adult Sex Distribution Child 030203 arthritis & rheumatology business.industry Infant Middle Aged medicine.disease Purpura Leukocytoclastic vasculitis Child Preschool HENOCH SCHONLEIN SYNDROME Age distribution Female medicine.symptom business |
| Zdroj: | Journal of clinical rheumatology : practical reports on rheumaticmusculoskeletal diseases. 22(2) |
| ISSN: | 1536-7355 |
| Popis: | Little attention has been so far paid to familial cases of Henoch-Schonlein syndrome. We performed a search of the Medical Subject Headings terms (Henoch or Schonlein OR anaphylactoid purpura OR IgA nephropathy OR Berger nephropathy) AND (family OR familial). We identified no more than 19 reports including 47 families with a total of 100 affected cases: their ages ranged from 1.3 to 51 years (median, 11 years), with a male-to-female ratio of 1.4. Familial cases developed simultaneously in 45% and nonsimultaneously in 55% of the families. Age, male-to-female ratio, and clinical findings were not statistically different in cases with simultaneous and nonsimultaneous familial occurrence of Henoch-Schonlein syndrome. Henoch-Schonlein syndrome occurs almost always sporadically. Age at presentation, male-to-female ratio, and findings are similar in familial (both simultaneously and nonsimultaneously occurring) and sporadic Henoch-Schonlein cases. |
| Databáze: | OpenAIRE |
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