Pleuropulmonary Blastoma
| Autor: | C, Granata, C, Gambini, C, Carlini, P, Repetto, M, Torre, C, Mazzola, G, Mattioli, V, Jasonni |
|---|---|
| Rok vydání: | 2001 |
| Předmět: |
Male
Lung Neoplasms Pleural Neoplasms Antineoplastic Agents therapeutic use Chemotherapy Adjuvant Child Preschool Dactinomycin therapeutic use Disease-Free Survival Humans Ifosfamide therapeutic use Lung Neoplasms drug therapy/pathology/surgery Male Pleural Neoplasms drug therapy/pathology/surgery Pneumonectomy Pulmonary Blastoma drug therapy/pathology/surgery Vincristine therapeutic use Disease-Free Survival Chemotherapy Adjuvant Vincristine Child Preschool drug therapy/pathology/surgery Pediatrics Perinatology and Child Health Dactinomycin Chemotherapy Humans Surgery Ifosfamide Child Preschool Pneumonectomy Pulmonary Blastoma Adjuvant |
| Zdroj: | European Journal of Pediatric Surgery. 11:271-273 |
| ISSN: | 1439-359X 0939-7248 |
| Popis: | We report a rare case of pleuropulmonary blastoma arising in a 3-year-old boy and involving the middle and upper lobes of the right lung. Radical resection of the mass was achieved by a bilobectomy. Microscopic examination of the histologic sections showed the typical findings of blastemal and mesenchymal areas with focal zones of rhabdomyoblastic and liposarcomatous differentiation. Monthly cycles of chemotherapy consisting of ifosfamide, vincristine and actinomycin D were given for 10 months after surgical resection. Our patient is presently alive and disease-free two years after diagnosis. As complete tumour ablation is essential to prevent local recurrence and allow any chance of survival, the favourable outcome of our patient is probably due to the radical resection of the neoplasm. |
| Databáze: | OpenAIRE |
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