Retinal Vasculitis Associated With Dermatomyositis Treated With Intravenous Steroids
| Autor: | Rula A. Hajj-Ali, Kimberly Baynes, Sunil K. Srivastava, Jawad Arshad, Careen Y. Lowder, Austen N. Knapp, Daniel F. Martin |
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| Rok vydání: | 2021 |
| Předmět: | |
| Zdroj: | J Vitreoretin Dis |
| ISSN: | 2474-1272 2474-1264 |
| Popis: | Purpose: This work aims to present treatment and long-term follow-up of a 31-year-old woman with dermatomyositis who presented with hemorrhagic retinal vasculitis and macular edema. Methods: A retrospective case report is presented. Results: A 31-year-old woman with dermatomyositis treated with systemic immunosuppression was evaluated for acute, reduced vision. Best-corrected visual acuity was hand motion in the right eye and 20/200 in the left eye. Fundus examination revealed diffuse intraretinal hemorrhages, cotton-wool spots, and vascular sheathing with a frosted branch angiitis–like appearance. Optical coherence tomography revealed significant macular edema and subretinal fluid that quickly resolved after admission and treatment with intravenous steroids. Multimodal imaging at 7-year follow-up disclosed long-term sequelae including peripheral nonperfusion and retinal neovascularization. Conclusions: When vasculitis associated with dermatomyositis is treated aggressively with intravenous steroids at initial presentation, good visual acuity outcomes can be achieved, but long-term consequences of retinal nonperfusion and neovascularization persist. |
| Databáze: | OpenAIRE |
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