Pulmonary vein stenosis: Case report and literature review
| Autor: | N Sweezey, Y Moayedi, S Kwon, R Amin |
|---|---|
| Rok vydání: | 2009 |
| Předmět: |
Pulmonary and Respiratory Medicine
medicine.medical_specialty Cardiac Catheterization medicine.medical_treatment Hypertension Pulmonary Case Report Constriction Pathologic Constriction Diseases of the respiratory system Lethargy Internal medicine Medicine Intubation Humans Pulmonary vein stenosis Cardiac catheterization Ultrasonography RC705-779 Respiratory distress business.industry Infant medicine.disease Pulmonary hypertension Treatment Outcome Pulmonary Veins Cardiology Female Presentation (obstetrics) business |
| Zdroj: | Canadian Respiratory Journal, Vol 16, Iss 6, Pp e77-e80 (2009) |
| ISSN: | 1916-7245 |
| Popis: | BACKGROUND: Pulmonary vein stenosis is a rare cause of pulmonary hypertension, with variable onset and presentation. One or more of the four pulmonary veins can be primarily or secondarily affected. A five-month-old girl presented with respiratory distress, lethargy and cyanosis requiring intubation.METHODS: Echocardiography showed right ventricular dilation, a right ventricular systolic pressure of 97 mmHg, decreased ejection fraction and turbulent flow at the left atrium. Cardiac catheterization revealed stenosis of the left-sided pulmonary veins, for which she underwent a Coles procedure.RESULTS: Postoperatively, there was a transient improvement in the patient’s pulmonary hypertension but she subsequently deteriorated. Her prognosis was considered bleak, and a decision was made with the family to withdraw care.CONCLUSION: Pulmonary vein stenosis is a rare cause of pulmonary hypertension, and is associated with significant morbidity and mortality. Surgical intervention may be of benefit in selected cases. It stands to reason that any treatment will have the best chance of success if completed before the pulmonary hypertension becomes fixed. Early diagnosis depends on a high index of clinical suspicion. |
| Databáze: | OpenAIRE |
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