Postoperative disseminated intravascular coagulation in a pregnant patient with Blue Rubber Bleb Nevus Syndrome presenting with acute intestinal obstruction: Case report and literature review
| Autor: | Celso de Oliveira Bernini, Edivaldo Massazo Utiyama, Carlos Augusto Metidieri Menegozzo, Newton Djin Mori, Fernando da Costa Ferreira Novo |
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| Rok vydání: | 2017 |
| Předmět: |
Disseminated intravascular coagulation
medicine.medical_specialty business.industry Pregnant patient Oligohydramnios Emergency department medicine.disease Article Blue rubber bleb nevus syndrome Surgery OBSTRUÇÃO DA SAÍDA GÁSTRICA 03 medical and health sciences 0302 clinical medicine Intestinal obstruction 030220 oncology & carcinogenesis Intussusception (medical disorder) medicine 030211 gastroenterology & hepatology Presentation (obstetrics) business Intussusception Blue Rubber Bleb Nevus Syndrome Coagulation Disorder |
| Zdroj: | Repositório Institucional da USP (Biblioteca Digital da Produção Intelectual) Universidade de São Paulo (USP) instacron:USP International Journal of Surgery Case Reports |
| Popis: | Highlights • BRBNS most commonly manifests as bleeding, however complications such as obstruction and infarction may be present. • In obstructive complications, with lesions deffusely present, surgical treatment without resection is a viable alternative. • DIVC should be promptly detected in such patients during the postoperative course. Although rare, it is a life-threatening condition. Background Blue Rubber Bleb Nevus Syndrome (BRBNS) is a rare condition which usually manifests as multiple hemangioma-like skin and gastrointestinal lesions. The latter often present with chronic bleeding. There is no consensus regarding the optimal management of such patients. Although rare, complications such as intestinal intussusception might occur, demanding surgical treatment. Postoperative complications such as coagulation disorders can increase morbidity and should be timely addressed. This is the first report of a life-threatening postoperative disseminated intravascular coagulation in such patients. The main objectives of this case report are to present diagnostic and treatment features of this condition and, more importantly, address the optimal management of postoperative disseminated intravascular coagulation. Case presentation Twenty-five year-old female pregnant patient presents to the emergency department with colicky pain and oligohydramnios. After C-section, persistent symptoms and further investigation led to the diagnosis of intestinal intussusception. After surgical management she showed clinical and laboratory signs of disseminated intravascular coagulation (DIVC), which was corrected with transfusional therapy and intraperitoneal clot evacuation. After optimal management, she was discharged home. Sirolimus was initiated further improving her condition. Conclusion This rare presentation of acute intestinal intussusception in a patient with Blue Rubber Bleb Nevus Syndrome was further complicated with postoperative coagulation disorder. Prompt surgical evaluation is essential especially when complications are suspected. Operative treatment might be necessary in the emergent setting. Close monitoring of infectious and coagulation parameters is essential in the postoperative period, and aggressive treatment should be timely initiated when disseminated intravascular coagulation is suspected. |
| Databáze: | OpenAIRE |
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