The First Case of Eosinophilic Granulomatosis with Polyangiitis Simultaneously Demonstrating Various Clinical Manifestations with Retroperitoneal Fibrosis and Membranous Nephropathy
| Autor: | Fumihiko Hinoshita, Isao Kondo, Daisuke Katagiri, Emi Sakamoto, Yohei Arai |
|---|---|
| Rok vydání: | 2021 |
| Předmět: |
medicine.medical_specialty
retroperitoneal fibrosis Case Report Disease Churg-Strauss Syndrome 030204 cardiovascular system & hematology Retroperitoneal fibrosis Glomerulonephritis Membranous Gastroenterology 03 medical and health sciences 0302 clinical medicine Membranous nephropathy Internal medicine Eosinophilic Internal Medicine medicine Humans Hydronephrosis business.industry Remission Induction Granulomatosis with Polyangiitis membranous nephropathy General Medicine medicine.disease eosinophilic granulomatosis with polyangiitis Disease category 030211 gastroenterology & hepatology simultaneous onset medicine.symptom business Granulomatosis with polyangiitis Nephrotic syndrome |
| Zdroj: | Internal Medicine |
| ISSN: | 1349-7235 0918-2918 |
| DOI: | 10.2169/internalmedicine.6399-20 |
| Popis: | The first case of eosinophilic granulomatosis with polyangiitis (EGPA) simultaneously demonstrating various clinical manifestations, including retroperitoneal fibrosis (RPF) causing hydronephrosis and membranous nephropathy (MN) leading to nephrotic syndrome, is presented. There have been no previous case reports demonstrating the simultaneous onset of these three disease categories with significant complex pathologies. This case was successfully managed by providing adequate combination therapies according to each disease category, leading to complete remission (CR) of all three diseases. In conclusion, we believe this case is extremely rare and clinically suggestive, and that these findings can be applied to a future phenotype-tailored treatment strategy for EGPA. |
| Databáze: | OpenAIRE |
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