Bleeding from cavernous angiomatosis of the rectum in Klippel-Trenaunay syndrome: report of three cases and literature review
| Autor: | Louis M. Wong Kee Song, Marcello Ferrara, Candace L. Wilson, Heidi K. Chua, Roger R. Dozois, Vandana Nehra, Richard M. Devine |
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| Rok vydání: | 2001 |
| Předmět: |
Adult
Male Angiomatosis Klippel-Trenaunay-Weber Syndrome medicine.medical_specialty Klippel-Trenaunay syndrome medicine.medical_treatment Rectum Angioma medicine Humans Coloanal anastomosis Hepatology Abdominoperineal resection Vascular disease Proctocolectomy business.industry Gastroenterology medicine.disease Surgery Rectal Diseases medicine.anatomical_structure Female Gastrointestinal Hemorrhage business |
| Zdroj: | The American Journal of Gastroenterology. 96:2783-2788 |
| ISSN: | 1572-0241 0002-9270 |
| DOI: | 10.1111/j.1572-0241.2001.04110.x |
| Popis: | Klippel-Trenaunay syndrome (KTS) is a congenital vascular anomaly characterized by limb hypertrophy, cutaneous hemangiomas, and varicosities. GI hemorrhage is a potentially serious complication secondary to diffuse hemangiomatous involvement of the gut. We report on three patients with KTS who presented with transfusion-dependent anemia and life-threatening bleeding due to extensive cavernous hemangiomas involving the rectum. Two patients were treated by proctocolectomy and coloanal anastomosis, which preserved anal function while controlling bleeding. The third patient required an abdominoperineal resection because of extensive rectal, perianal, and perineal angiomatosis. The literature on the evaluation and management of GI hemorrhage in KTS, particularly of colorectal origin, is reviewed. |
| Databáze: | OpenAIRE |
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