Oral Management of a Haematopoietic Stem Cell Transplant Recipient with Chédiak–Higashi Syndrome

Autor:	Nozomi Ito, Gaku Koizumi, Kazuto Kurohara, Miho Hayashi, Kokoro Hamada, Naoya Arai, Kasumi Shimizu
Jazyk:	angličtina
Rok vydání:	2021
Předmět:	integumentary system business.industry Abnormal bleeding Chédiak–Higashi syndrome Case Report RK1-715 medicine.disease Transplantation Haematopoiesis hemic and lymphatic diseases Dentistry Immunology medicine Albinism Aggressive periodontitis Stem cell business General Dentistry Immunodeficiency
Zdroj:	Case Reports in Dentistry, Vol 2021 (2021) Case Reports in Dentistry
ISSN:	2090-6455 2090-6447
Popis:	Chédiak–Higashi syndrome (CHS), a rare autosomal recessive disorder associated with leukocyte dysfunction, is characterised by partial skin and hair albinism, immunodeficiency, and abnormal bleeding. Furthermore, it may be associated with cognitive and neurological impairments. The long-term prognosis of patients is generally poor, and haematopoietic stem cell transplantation is a radical immunodeficiency treatment. Here, we report a case of successful oral management of an 18-year-old woman with CHS accompanied by aggressive periodontitis who underwent haematopoietic stem cell transplantation.
Databáze:	OpenAIRE
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