Pleural Epithelioid Hemangioendothelioma: Literature Summary and Novel Case Report
| Autor: | Andrew I. Ritchie, Julita Salijevska, Francisco Mauri, David Adeboyeku, Amy Clifford, Robert Watson |
|---|---|
| Jazyk: | angličtina |
| Rok vydání: | 2015 |
| Předmět: |
Pulmonary hemangioendothelioma
medicine.medical_specialty Intravascular bronchoalveolar tumor business.industry Cancer Case Report General Medicine Chest pain medicine.disease Symptomatic relief Surgery Pleural drainage medicine Pleura Radiology Epithelioid hemangioendothelioma medicine.symptom Presentation (obstetrics) Differential diagnosis business Pleural Epithelioid Hemangioendothelioma |
| Zdroj: | Journal of Clinical Medicine Research |
| ISSN: | 1918-3011 1918-3003 |
| Popis: | Epithelioid hemangioendothelioma (EHE) is a rare malignant cancer of vascular origin that can affect multiple and varied tissue sites. A subtype of EHE, pulmonary epithelioid hemangioendothelioma (PHE), is more unusual with only 200 reported cases. Of these, only 27 have been classified as pleural in origin. Based on available literature, the average age of presentation of pleural PHE is 45.7 years with a male preponderance of 2.375. A summary of all published case reports reveals significant heterogeneity both in presentation and management. Here we add to this knowledge-base with a report of an unusual case of pleural PHE in a 36-year-old female who presented with a 6-week history of chest pain and breathlessness. Significant challenges in the diagnosis and management of patients with pleural PHE exist, including a wide initial differential diagnosis and difficulties in obtaining tissue specimens, coupled with relatively limited treatment options. Early referral to a cardiothoracic center for video-assisted thoracoscopic biopsy is crucial in facilitating a diagnosis and allowing adequate pleural drainage for symptomatic relief. J Clin Med Res. 2015;7(7):566-570 doi: http://dx.doi.org/10.14740/jocmr2174w |
| Databáze: | OpenAIRE |
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