Peroral Endoscopic Myotomy in Diffuse Thickened Esophageal Wall in an Adolescent

Autor: A.A. Smirnov, Aleksandr N Burakov, Kirill D Semenikhin, Egor V Blinov, Sergey Y Dvoreckij, Nadezhda V Konkina, Aleksandr N Shvetsov
Rok vydání: 2018
Předmět:
Zdroj: Case Reports in Gastroenterology, Vol 12, Iss 2, Pp 497-503 (2018)
Case Reports in Gastroenterology
ISSN: 1662-0631
DOI: 10.1159/000492212
Popis: Achalasia is an extremely rare pathology in children. Peroral endoscopic myotomy (POEM) is the gold standard for the surgical treatment of achalasia in adults, but only a limited number of cases of achalasia treatment using POEM in children have been published in the literature. Sometimes, high-resolution manometry signs of achalasia can mimic diffuse esophageal leiomyoma. This case report represents the first known successful performance of POEM on a 15-year-old female with diffuse thickening of the esophagus with signs and symptoms of achalasia and suspicion for Alport syndrome associated with diffuse esophageal leiomyoma.
Databáze: OpenAIRE