Inspiratory muscle strength training improves lung function in patients with the hypermobile Ehlers–Danlos syndrome: A randomized controlled trial

Autor: Trinh Hermanns-Lê, Gregory Reychler, Daniel Manicourt, Gérald Pierard, Giuseppe Liistro
Přispěvatelé: UCL - SSS/DDUV/GEHU - Génétique, UCL - SSS/IREC/PNEU - Pôle de Pneumologie, ORL et Dermatologie, UCL - (SLuc) Service de pneumologie
Rok vydání: 2018
Předmět:
Zdroj: American Journal of Medical Genetics. Part A, Vol. 179, no. 3, p. 356-364 (2019)
ISSN: 1552-4833
1552-4825
Popis: As exertional inspiratory dyspnea is a common disabling complaint in hypermobile Ehlers-Danlos syndrome (hEDS) often also known as joint hypermobility syndrome (JHS), we investigated inspiratory muscle (IM) strength in patients with hEDS, and we assessed the effects of IM training (IMT) on IM strength, lung function, and exercise capacity. A prospective evaluation of IM strength followed by a randomized controlled trial of IMT was performed in women with hEDS. Sniff nasal inspiratory pressure (SNIP) was used to routinely measure IM strength and IMT was carried out using a pressure threshold device. IM strength (main outcome), cardiopulmonary function, exercise capacity, and emotional distress of both the treated and control groups were evaluated at the start and at the end of the 6-week training period. IM strength was reduced (
Databáze: OpenAIRE