Angiomatoid Fibrous Histiocytoma With Paraneoplastic Platelet Storage Pool Deficiency
| Autor: | Jennifer D. Elster, Lerraughn M. Morgan, Susan Coventry, Emily R. Miller, Ashok Raj |
|---|---|
| Rok vydání: | 2017 |
| Předmět: |
Platelet Storage Pool Deficiency
Pathology medicine.medical_specialty medicine.medical_treatment Soft Tissue Neoplasms Histiocytoma Malignant Fibrous 030204 cardiovascular system & hematology Lesion Diagnosis Differential 03 medical and health sciences 0302 clinical medicine Hematoma Incision and drainage Medicine Humans Child Platelet storage pool deficiency business.industry Angiomatoid fibrous histiocytoma Soft tissue medicine.disease Primary tumor Bleeding diathesis Treatment Outcome Thigh 030220 oncology & carcinogenesis Pediatrics Perinatology and Child Health Female medicine.symptom business |
| Zdroj: | Pediatrics. 141(3) |
| ISSN: | 1098-4275 |
| Popis: | Angiomatoid fibrous histiocytoma is a rare soft tissue tumor usually discovered in young individuals. This tumor is often mistaken for a hematoma and typically misdiagnosed. It is commonly found in the extremities and may be associated with a site of recent or previous trauma. Characteristic histology includes nodules of histiocytoid spindle cells with pseudoangiomatoid spaces, fibrous pseudocapsules, and lymphoid cuffing. We describe the case of an 8-year-old girl who presented after incision and drainage of a superficial thigh lesion and experienced subsequent chronic bleeding of her wound. Her initial presentation was concerning for an underlying bleeding disorder, and laboratory analysis uncovered a paraneoplastic platelet function disorder that resolved with therapy of the primary tumor. |
| Databáze: | OpenAIRE |
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