Erythropoietic Protoporphyria Presenting as Hydroa Aestivale
| Autor: | Allan G. Redeker, Ronald S. Bronow |
|---|---|
| Rok vydání: | 1964 |
| Předmět: |
medicine.medical_specialty
Erythrocytes Porphyrins Adolescent Protoporphyria Erythropoietic Keratosis Genetics Medical Dermatology Urine Hydroa aestivale Feces Porphyrias chemistry.chemical_compound Diseases in Twins medicine Humans Photosensitivity Disorders Child integumentary system business.industry General Medicine medicine.disease Blood Porphyria chemistry Hydroa Vacciniforme Hydroa vacciniforme Protoporphyrin Erythropoietic protoporphyria business |
| Zdroj: | Archives of Dermatology. 89:104 |
| ISSN: | 0003-987X |
| DOI: | 10.1001/archderm.1964.01590250110019 |
| Popis: | Three patients with erythropoietic protoporphyria, the first to be reported from this country, have been studied. In each, as in the cases reported from Europe, marked elevations of the free erythrocyte and fecal protoporphyrin levels were found. However, the photocutaneous eruption, observed in all three patients, is considered to result from the high level of protoporphyrin found in the plasma. The cutaneous features were those of hydroa aestivale, and it is proposed that hydroa aestivale is a form of erythropoietic protoporphyria. |
| Databáze: | OpenAIRE |
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