Convulsive syncope resulting from arrhythmia in a case of congenital deafness with ECG abnormalities
| Autor: | A.N.P. van Heyst, J. Sebus, H.W. van Bruggen |
|---|---|
| Jazyk: | angličtina |
| Rok vydání: | 1969 |
| Předmět: |
medicine.medical_specialty
Deafness Ventricular tachycardia Convulsive syncope Syncope Geneeskunde Electrocardiography Internal medicine medicine Humans Hyperuricemia cardiovascular diseases Child business.industry Unconsciousness Arrhythmias Cardiac medicine.disease Ventricular Fibrillation Diabetes insipidus Ventricular fibrillation Circulatory system Cardiology cardiovascular system Female medicine.symptom Cardiology and Cardiovascular Medicine business Atrial flutter Adams-Stokes Syndrome |
| Zdroj: | American Heart Journal, 78(1), 81. Elsevier |
| ISSN: | 0002-8703 |
| Popis: | A description is given of an 8-year-old girl with the syndrome of Jervell and Lange Nielsen consisting of congenital deafness, prolonged Q-T time in the ECG, and attacks of unconsciousness. In addition there were extrasystoles, ventricular tachycardia, ventricular fibrillation, and atrial flutter. The syncopes proved to be based on circulatory insufficiency as a result of ventricular fibrillation. The child suffered in addition from diabetes insipidus on the basis of a disturbance in renal function, and hyperuricemia was repeatedly found. The girl died as a result of an attack of ventricular fibrillation, after an initial period of considerable clinical improvement upon Benemid medication. It is suggested that the recently described combination of Q-T prolongation in the ECG and syncopal attacks as a result of ventricular fibrillation must be regarded as the same genotypical entity. The possibility is mentioned that this case may have presented a symptom complex in association with hyperuricemia. |
| Databáze: | OpenAIRE |
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