Hyper IgE Disorder Associated with Multiple Fused Primary Teeth: A Rare Clinical Occurrence
| Autor: | Samata Y, Reddy Ks, Kumar Mm, Sankar As |
|---|---|
| Jazyk: | angličtina |
| Rok vydání: | 2010 |
| Předmět: |
Pediatrics
medicine.medical_specialty medicine.drug_class Antibiotics Orthodontics Case Report Syndrome Skin infection Immunoglobulin E Hyperimmunoglobulin medicine biology Dentition business.industry Pneumonia medicine.disease Penicillin Job Syndrome Pediatrics Perinatology and Child Health biology.protein Periodontics Oral Surgery Hyperimmunoglobulin E syndrome business medicine.drug |
| Zdroj: | International Journal of Clinical Pediatric Dentistry |
| ISSN: | 0975-1904 0974-7052 |
| Popis: | The hyperimmunoglobulin E syndrome (HIES) is a multisystem disorder that affects the dentition, skeleton, connective tissues and immune system. Little is known about oral manifestations of the syndrome. The purpose of this report was to describe a 6-year-old boy with suspected autosomal recessive HIES syndrome who had multiple fused primary teeth, which is a rare association with JOB syndrome. The patient gave a history of pneumonia and skin infections. Recognition of such case at an early age is necessary to reduce morbidity. As conclusion, treatment for this condition is life long administration of therapeutic doses of penicillinase-resistant penicillin, with the addition of other antibiotics or antifungal agents as required for specific infections. |
| Databáze: | OpenAIRE |
| Externí odkaz: |
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