Familial 'benign' pemphigus? Erythroderma and fatal outcome
| Autor: | Paula Baldissera Tansini, Renan Rangel Bonamigo, Magda Blessmann Weber, Ana Letícia Boff |
|---|---|
| Jazyk: | angličtina |
| Rok vydání: | 2020 |
| Předmět: |
medicine.medical_specialty
Fatal outcome Maceration (bone) Vesiculobullous Erythroderma Case Report Disease Dermatology Pemphigus benign familial 030207 dermatology & venereal diseases 03 medical and health sciences 0302 clinical medicine medicine Pênfigo familiar benigno skin and connective tissue diseases Dermatite esfoliativa Dermatitis exfoliative Unusual case Relatos de casos integumentary system business.industry Genodermatosis medicine.disease Skin diseases Skin diseases vesiculobullous 030220 oncology & carcinogenesis Familial Benign Pemphigus RL1-803 business |
| Zdroj: | Anais Brasileiros de Dermatologia, Vol 95, Iss 1, Pp 75-77 (2020) Repositório Institucional da UFRGS Universidade Federal do Rio Grande do Sul (UFRGS) instacron:UFRGS Anais Brasileiros de Dermatologia |
| ISSN: | 0365-0596 |
| Popis: | Hailey-Hailey disease, or familial benign pemphigus, is a rare bullous genodermatosis that usually presents with flaccid blisters, erosions, and maceration limited to flexural areas, resulting in increased morbidity and reduced quality of life for affected patients. The authors report an unusual case of generalized Hailey-Hailey disease with erythroderma and fatal outcome. |
| Databáze: | OpenAIRE |
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