Multiple primary chordomas of the lung

Autor: Takayuki Shiina, Kazuo Yoshida, Hisashi Shimojo, Maki Ohya
Rok vydání: 2018
Předmět:
musculoskeletal diseases
Pulmonary and Respiratory Medicine
medicine.medical_specialty
Axial skeleton
Radiography
Case Report
Computed tomography
Asymptomatic
FDG-PET
fluorine-18 fluorodeoxyglucose positron emission tomography

03 medical and health sciences
0302 clinical medicine
Chordoma
Medicine
Lung
Benign notochordal cell tumor
Pathological
lcsh:RC705-779
AFP
alpha-fetoprotein

medicine.diagnostic_test
business.industry
lcsh:Diseases of the respiratory system
Brachyury
BNCT
benign notochordal cell tumor

CT
computed tomography

medicine.anatomical_structure
030228 respiratory system
030220 oncology & carcinogenesis
H&E
hematoxylin and eosin

Radiology
CEA
carcinoembryonic antigen

Abnormality
medicine.symptom
IL-2R
interleukin-2 receptor

business
Chest radiograph
hCG
human chorionic gonadotrophin
Zdroj: Respiratory Medicine Case Reports, Vol 25, Iss, Pp 142-144 (2018)
Respiratory Medicine Case Reports
ISSN: 2213-0071
DOI: 10.1016/j.rmcr.2018.08.012
Popis: We here report the case of a 40-year-old man with primary pulmonary chordomas. Although an abnormality had been noted on a chest radiograph at age 26 years, the patient had not undergone further examination at that time because he was asymptomatic. Standard chest radiographs and computed tomography showed slow-growing, multiple bilateral pulmonary nodules. Two tumors were resected thoracoscopically to obtain a diagnosis. Pathologic examination resulted in a diagnosis of chordomas. Subsequent systemic examination revealed no additional lesions, not even in the axial skeleton. The patient is alive without any new lesions 38 months after surgery. These clinical and pathological findings suggest that our patient has multiple primary chordomas of the lung, which is an extremely rare condition. Keywords: Chordoma, Lung, Brachyury, Benign notochordal cell tumor
Databáze: OpenAIRE