Pulmonary arterial hypertension in adult onset Still’s disease: a case report of a severe complication
| Autor: | A. Foucher, L. Guilleminault, F. Paganin, P. Poubeau, S. Laurent |
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| Rok vydání: | 2016 |
| Předmět: |
Adult
Pulmonary and Respiratory Medicine Pathology medicine.medical_specialty Adult-onset Still's disease Pediatrics Hypertension Pulmonary Case Report Disease 030204 cardiovascular system & hematology Pulmonary arterial hypertension Auto inflammatory disease Tadalafil Young Adult 03 medical and health sciences 0302 clinical medicine Adrenal Cortex Hormones medicine Humans Young adult Antihypertensive Agents Severe complication 030203 arthritis & rheumatology Adult onset Still’s disease Phenylpropionates business.industry Auto-inflammatory disease medicine.disease Pulmonary hypertension Pyridazines Interleukin 1 Receptor Antagonist Protein Echocardiography Antirheumatic Agents Female Tomography X-Ray Computed business Still's Disease Adult-Onset medicine.drug |
| Zdroj: | BMC Pulmonary Medicine |
| ISSN: | 1471-2466 |
| DOI: | 10.1186/s12890-016-0237-x |
| Popis: | Background Adult onset of Still’s disease (AOSD) is a rare systemic inflammatory disease. Cardiorespiratory complications are mainly represented by pleural and pericardial disorders and are less frequent than cutaneous and articular complaints. Pulmonary arterial hypertension (PAH) occurring in AOSD is rarely described in literature. Case presentation We present the case of a young patient who developed severe PAH 2 years after diagnosis of AOSD. This is a rare and severe complication which is probably underestimated. Conclusions PAH in AOSD can be lethal, and unfortunately its occurrence is unpredictable. Echocardiographic screening of AOSD patients should be evaluated in further trials. Currently, the most suitable treatment is still unknown. Electronic supplementary material The online version of this article (doi:10.1186/s12890-016-0237-x) contains supplementary material, which is available to authorized users. |
| Databáze: | OpenAIRE |
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