Congenital pulmonary vein stenosis: Structural changes in a patient with normal pulmonary artery wedge pressure
| Autor: | Dwight T. Tuuri, Lynne Reid, Robert L. Geggel, Donald C. Fyler, Ruthellen Fried |
|---|---|
| Rok vydání: | 1984 |
| Předmět: |
Male
medicine.medical_specialty Cardiac Catheterization Pulmonary Circulation Hypertension Pulmonary Autopsy Constriction Pathologic Pulmonary Artery Internal medicine Medicine Humans Pulmonary Wedge Pressure Pulmonary vein stenosis Vein Pulmonary wedge pressure Lung business.industry Infant medicine.disease Venous Obstruction Stenosis medicine.anatomical_structure Pulmonary Veins Cardiology Congenital pulmonary vein stenosis business Cardiology and Cardiovascular Medicine Lower limbs venous ultrasonography |
| Zdroj: | Journal of the American College of Cardiology. 3(1):193-199 |
| ISSN: | 0735-1097 |
| DOI: | 10.1016/s0735-1097(84)80447-7 |
| Popis: | A male infant is described who died at 13 months of age with stenosis of all extrapulmonary veins except the left upper vein. The pulmonary artery wedge pressure was normal, the first time this is reported in this condition. At autopsy, there were structural changes of the pulmonary arteries and veins in all lobes with or without pulmonary vein stenosis. Arterial changes—muscle extension, medial hypertrophy and decreased arterial size— analyzed quantitatively were found to be similar in all lobes. Venous medial hypertrophy was more marked in obstructed lobes. These anatomic changes are presumably due to fixed venous obstruction in the pulmonary lobes drained by stenotic veins and to high flow in the left upper lobe. |
| Databáze: | OpenAIRE |
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