How Could Aortic Atresia With Interrupted Aortic Arch Survive? About a Neonatal Repair on Two Ventricles

Autor: Pranav Subbaraya Kandachar, Abdullah Al-Bulushi, Madan Mohan Maddali, François Lacour-Gayet
Rok vydání: 2019
Předmět:
Pulmonary and Respiratory Medicine
medicine.medical_specialty
Double aortic arch
Vascular Malformations
Heart Ventricles
Aortic Diseases
Aorta
Thoracic

030204 cardiovascular system & hematology
Norwood Procedures
Lesion
03 medical and health sciences
0302 clinical medicine
medicine.artery
Internal medicine
Humans
Medicine
cardiovascular diseases
Aortic atresia
Cardiac Surgical Procedures
Aorta
business.industry
Bilateral patent ductus arteriosus
Cardiovascular Surgical Procedures
Interrupted aortic arch
Infant
Newborn

Aberrant right subclavian artery
General Medicine
medicine.disease
Coronary arteries
medicine.anatomical_structure
030228 respiratory system
Descending aorta
cardiovascular system
Cardiology
Female
Surgery
medicine.symptom
Cardiology and Cardiovascular Medicine
business
Vascular Surgical Procedures
Zdroj: Seminars in Thoracic and Cardiovascular Surgery. 31:118-121
ISSN: 1043-0679
DOI: 10.1053/j.semtcvs.2018.07.009
Popis: Aortic atresia with interrupted aortic arch (IAA) is an exceptional condition. In absence of associated lesion, the flow to the brain and the retrograde flow to the coronary arteries can only come from vessels on the descending aorta. This flow needs to be large enough to supply the brain and the myocardium. The only IAA type compatible with survival is type C where the flow from descending aorta could be insured by the left carotid and the left vertebral artery, branch of the left subclavian artery. Only one such a case was described in the literature. All the other surviving cases had an associated lesion including: a double aortic arch, an aorto-pulmonary window (AP window), an aberrant right subclavian artery or a bilateral patent ductus arteriosus (PDA). We report a case of aortic atresia with IAA type B associated with a double aortic arch that underwent a successful bi-ventricular one-stage neonatal Norwood-Rastelli repair and is doing well after 18 months.
Databáze: OpenAIRE