Self-healing juvenile cutaneous mucinosis, a sclerodermoid disorder simulating juvenile dermatomyositis: a case-based review
| Autor: | Keshavamurthy Vinay, Amrinder J. Kanwar, Ankur Kumar Jindal, Surjit Singh, Gummadi Anjani, Sunil Dogra, Pratap Kumar Patra, Anuradha Bishnoi, Debajyoti Chatterjee |
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| Rok vydání: | 2020 |
| Předmět: |
Male
medicine.medical_specialty Mucinoses Immunology Periorbital Edema Arthritis Dermatomyositis Diagnosis Differential 03 medical and health sciences 0302 clinical medicine Rheumatology Internal medicine Scleromyxedema medicine Immunology and Allergy Juvenile Humans 030212 general & internal medicine Self-healing juvenile cutaneous mucinosis Juvenile dermatomyositis Skin 030203 arthritis & rheumatology business.industry medicine.disease Dermatology Mucinosis Child Preschool Female business |
| Zdroj: | Rheumatology international. 40(11) |
| ISSN: | 1437-160X |
| Popis: | Self-healing juvenile cutaneous mucinosis (SHJCM) is a rare childhood disease with characteristic cutaneous and rheumatic manifestations. Cutaneous manifestations include a combination of nodules affecting peri-articular (especially interphalangeal joints) and head and neck areas; and linearly arranged ivory white papules over an erythematous indurated skin. Despite a benign course, an abrupt onset of symptoms with extensive cutaneous involvement often leads to parental anxiety, overenthusiastic evaluation and sometimes aggressive treatment. A peculiar cutaneous distribution in SHJCM including nodular lesions and periorbital edema, arthritis and arthralgia in a few cases, may simulate juvenile dermatomyositis. It is, therefore, important for dermatologists and pediatricians to be aware of this entity. In this report, we describe two cases of SHJCM and briefly review similarly reported cases in children. |
| Databáze: | OpenAIRE |
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