Portal cavernoma cholangiopathy: diagnosis, imaging, and intervention
Autor: | Lauren N Moomjian, Sarah G Winks |
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Rok vydání: | 2016 |
Předmět: |
medicine.medical_specialty
Biliary Tract Diseases Urology Portal venous pressure Constriction Pathologic 030218 nuclear medicine & medical imaging Diagnosis Differential 03 medical and health sciences 0302 clinical medicine Internal medicine medicine Humans Radiology Nuclear Medicine and imaging Vascular Diseases Radiological and Ultrasound Technology Portal Vein business.industry Bile duct Gastroenterology Hepatology medicine.disease Thrombosis Portal vein thrombosis medicine.anatomical_structure Biliary tract Vascular Disorder Disease Progression 030211 gastroenterology & hepatology Radiology Hepatolithiasis business |
Zdroj: | Abdominal Radiology. 42:57-68 |
ISSN: | 2366-0058 2366-004X |
DOI: | 10.1007/s00261-016-0957-7 |
Popis: | The term portal cavernoma cholangiopathy refers to the biliary tract abnormalities that accompany extrahepatic portal vein obstruction (EHPVO) and subsequent cavernous transformation of the portal vein. EHPVO is a primary vascular disorder of the portal vein in children and adults manifested by longstanding thrombosis of the main portal vein. Nearly all patients with EHPVO have manifestations of portal cavernoma cholangiopathy, such as extrinsic indentation on the bile duct and mild bile duct narrowing, but the majority are asymptomatic. However, progressive portal cavernoma cholangiopathy may lead to severe complications, including secondary biliary cirrhosis. A spectrum of changes is seen radiologically in the setting of portal cavernoma cholangiopathy, including extrinsic indentation of the bile ducts, bile duct stricturing, bile duct wall thickening, angulation and displacement of the extrahepatic bile duct, cholelithiasis, choledocholithiasis, and hepatolithiasis. Radiologists must be aware of this disorder in order to provide appropriate imaging evaluation and interpretation, to facilitate appropriate treatment and to distinguish this entity from its potential radiologic mimics. |
Databáze: | OpenAIRE |
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