A 23-year-old patient with neurofibromatosis associated with acute myocardial infarction, vasospasm and a coronary artery ectasis

Autor: Masahiko Kinoshita, Mitsuhiro Kajinami, Toshimasa Kajinami, Nobuyuki Ohmichi, Naoko Ishimoto, Toshikazu Fuchi
Rok vydání: 1997
Předmět:
Zdroj: Internal medicine (Tokyo, Japan). 36(9)
ISSN: 0918-2918
Popis: We treated a 23-year-old male with neurofibromatosis with acute myocardial infarction. Cardiac catheterization revealed severe organic stenosis in the left anterior descending artery, an ectasic left circumflex artery and a small right coronary artery. Percutaneous transluminal coronary angioplasty (PTCA) was performed on the stenosis. In follow-up catheterizations, intracoronary administration of ergometrine induced vasospasm of the left coronary artery including at the PTCA site. An I 123 metaiodobenzylguanidine (MIBG) scintigram showed defects in the septum, inferior wall and apex. These findings suggest abnormality of the cardiac sympathetic nerve in neurofibromatosis.
Databáze: OpenAIRE