Primary cutaneous peripheral T-cell lymphoma, not otherwise specified, associated with lymphomatoid papulosis after a 9-year follow up: A case report
| Autor: | Masatoshi Jinnin, Ibu Matsuzaki, Nozomi Yonei, Shin-ichi Murata, Masakazu Fujimoto, Kyoko Muraoka, Yoshifumi Iwahashi |
|---|---|
| Rok vydání: | 2019 |
| Předmět: |
Male
medicine.medical_specialty Skin Neoplasms Exacerbation Biopsy Peripheral T-cell lymphoma not otherwise specified Dermatology Administration Cutaneous Cutaneous lymphoma Lesion 030207 dermatology & venereal diseases 03 medical and health sciences 0302 clinical medicine Fatal Outcome Lymphomatoid Papulosis hemic and lymphatic diseases medicine Humans Lymphomatoid papulosis Glucocorticoids Aged Skin Aged 80 and over Mycosis fungoides business.industry Not Otherwise Specified Lymphoma T-Cell Peripheral General Medicine Chemoradiotherapy medicine.disease Lymphoma Lymphoma T-Cell Cutaneous 030220 oncology & carcinogenesis Disease Progression medicine.symptom business Follow-Up Studies |
| Zdroj: | The Journal of dermatologyReferences. 47(6) |
| ISSN: | 1346-8138 |
| Popis: | Lymphomatoid papulosis (LyP) is a self-limiting cutaneous T-cell lymphoproliferative disorder that may progress into malignant lymphoma. Most of the previously reported associated lymphomas are primary cutaneous anaplastic large-cell lymphoma and mycosis fungoides with a low mortality rate. We report a case of primary cutaneous peripheral T-cell lymphoma, not otherwise specified (pcPTCL-NOS), associated with LyP after long-term follow up. The patient was a 79-year old Japanese man followed up for 9 years. He suddenly developed a 3-cm ulcerated lesion on his forehead, which was diagnosed as an exacerbation of LyP. The lesion regressed after conservative treatment, but the patient soon developed multifocal pcPTCL-NOS. Thereafter, the patient developed pneumonia and cerebral infarction and died within a few months of the onset of malignant lymphoma. Aggressive cutaneous lymphoma may develop in LyP patients. The present case re-emphasizes the need for careful follow up of patients with persistent LyP. |
| Databáze: | OpenAIRE |
| Externí odkaz: |
|
Plný text