Giant Pulmonary Artery Thrombotic Material, Due to Chronic Thromboembolic Pulmonary Hypertension, Mimics Pulmonary Artery Sarcoma
| Autor: | Paraskevi Trivilou, Dimitrios Iordanidis, Konstantinos Anagnostopoulos, Dionyssia Birmpa, Dimitrios Benas, Stylianos Argentos, Eckhard Mayer, Aikaterini Mpahara, Maria Mademli, Helen Triantafyllidi |
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| Rok vydání: | 2021 |
| Předmět: |
Medicine (General)
medicine.medical_specialty Respiratory distress business.industry medicine.medical_treatment pulmonary endarterectomy Case Report General Medicine medicine.disease Malignancy Thrombosis Pulmonary hypertension chronic thromboembolic pulmonary hypertension Pulmonary embolism R5-920 medicine.artery Internal medicine Pulmonary artery medicine Cardiology pulmonary artery sarcoma Sarcoma business Endarterectomy |
| Zdroj: | Medicina, Vol 57, Iss 992, p 992 (2021) Medicina |
| ISSN: | 1648-9144 |
| Popis: | In this article, we present the case of a 38-year-old female who suffered from serious respiratory distress. After an extensive pulmonary artery imaging diagnostic work-up (CTPA, MRA and PET), we were unable to differentiate between chronic thromboembolic pulmonary hypertension (CTEPH) vs. pulmonary artery sarcoma (PAS) due to extensive filling defects and extraluminal findings. Although surgery was postponed for nine months due to the COVID-19 pandemic, CTEPH diagnosis, due to a high-thrombus burden, was finally confirmed after pulmonary endarterectomy (PEA). Conclusively, imaging findings of rare cases of CTEPH might mimic PAS and the surgical removal of the lesion are both needed for a final diagnosis. What is Already Known about This Topic? Pulmonary artery sarcoma (PAS) is a rare but aggressive malignancy, which originates from the intimal layer of the pulmonary artery (PA); Chronic thromboembolic pulmonary hypertension (CTEPH) is based on chronic, organized flow-limiting thrombi inside PA circulation and subsequent pulmonary hypertension. What Does This Study Contribute? Since radiological findings of CTEPH cases might rarely mimic PAS, pulmonary artery endarterectomy and subsequent histopathologic study are needed for a final diagnosis. |
| Databáze: | OpenAIRE |
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