Limited dorsal myeloschisis associated with dermoid elements
| Autor: | Greg S. Moes, Sebastian Eibach, Dachling Pang, John Zovickian |
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| Rok vydání: | 2016 |
| Předmět: |
Dorsum
Adult Male Pathology medicine.medical_specialty Dermal Sinus Biology Primary neurulation Spinal Cord Diseases 03 medical and health sciences Fibrous stroma 0302 clinical medicine 030225 pediatrics otorhinolaryngologic diseases medicine Initial treatment Humans Neural Tube Defects Child Dermoid Cyst Infant Newborn Infant General Medicine Anatomy Middle Aged medicine.disease Myeloschisis Spinal cord medicine.anatomical_structure Dermoid cyst Child Preschool Pediatrics Perinatology and Child Health Female Neurology (clinical) 030217 neurology & neurosurgery |
| Zdroj: | Child's nervous system : ChNS : official journal of the International Society for Pediatric Neurosurgery. 33(1) |
| ISSN: | 1433-0350 |
| Popis: | Limited dorsal myeloschisis (LDM) originates from undisjointed neural and cutaneous ectoderms during primary neurulation. Its hallmark is a fibroneural stalk causing tethering on the dorsal spinal cord rostral to the conus. Its treatment is a relatively straightforward resection of the LDM stalk from the spinal cord. On reviewing our series of 75 cases of LDMs, we found that the majority of LDM stalks have only a glioneuronal core within a fibrous stroma, but a small number have been found to have elements of dermoid cyst or a complete dermal sinus tract either contiguous with the fibroneural stalk or incorporated within its glial matrix, not surprising considering the original continuum of cutaneous and neural ectoderm in LDMs’ embryogenesis. The dermoid element can be microscopic and escape casual observation, but could grow to large intradural dermoid cysts if part of the dermoid invested LDM stalk is left inside the dura. We present our series of LDMs associated with dermoid elements and recommend excising the entire length of the intradural LDM stalk from its dural entry point to its merge point with the spinal cord during the initial treatment to avoid secondary deterioration and additional surgery. |
| Databáze: | OpenAIRE |
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