Erdheim Chester disease: a rare cause of knee and leg pain
Autor: | R. Sistermann, B. D. Katthagen |
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Rok vydání: | 2000 |
Předmět: |
Male
medicine.medical_specialty Exophthalmos Long bone Pain Traumatology Osteosclerosis medicine Humans Knee Orthopedics and Sports Medicine Leg Granuloma business.industry Syndrome General Medicine Middle Aged medicine.disease Osteochondrodysplasia Surgery Radiography Histiocytosis medicine.anatomical_structure Diabetes insipidus Erdheim–Chester disease medicine.symptom business |
Zdroj: | Archives of Orthopaedic and Trauma Surgery. 120:112-113 |
ISSN: | 1434-3916 0936-8051 |
DOI: | 10.1007/pl00021229 |
Popis: | A case of Erdheim Chester disease in a 51-year-old Turkish patient is described. Erdheim Chester disease is a rare form of lipoid granulomatosis. Knee and leg pain are the most common symptoms, and physicians working in orthopaedics and traumatology are the first to be consulted. Our patient demonstrated a typical bilateral, symmetric sclerosis of the metaphyseal region of long bones of the lower extremity, histologic examination revealed foamy, lipid-loaded histiocytes. The patient also suffered from arterial hypertension, diabetes insipidus and exophthalmos of the left eye. The diagnosis was confirmed by a bone biopsy, and the patient was treated with non-steroidal anti-inflammatory drugs, corticosteroids and vincristine. |
Databáze: | OpenAIRE |
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