Persistent Sweet’s syndrome occurring in a child with a primary immunodeficiency
| Autor: | Jane L. Messina, Kimberly E. Lipp, Philip D. Shenefelt, Robert P. Nelson, Neil A. Fenske |
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| Rok vydání: | 1999 |
| Předmět: |
Cellular immunity
Neutrophils T-Lymphocytes Lymphocytosis Dermatology Lymphopenia Immunopathology medicine Humans Immunodeficiency Sweet's syndrome B-Lymphocytes business.industry Standard treatment Immunologic Deficiency Syndromes Histiocytes medicine.disease Sweet Syndrome Neutrophilia El Niño Child Preschool Immunology Primary immunodeficiency Female Epidermis medicine.symptom business |
| Zdroj: | Journal of the American Academy of Dermatology. 40:838-841 |
| ISSN: | 0190-9622 |
| DOI: | 10.1053/jd.1999.v40.a95650 |
| Popis: | Sweet’s syndrome (SS) occurs most commonly in association with inflammatory or neoplastic disorders. Only rarely has it been associated with immunodeficiency disorders. We describe a child with a T-cell immunodeficiency who had a persistent neutrophilic dermatosis that was histologically and clinically consistent with SS. SS associated with immunodeficiencies may occur as a reaction to an underlying infection or a defect in immunoregulation. Such patients, however, may not be able to produce the classic fever and neutrophilia associated with SS. They may fail to respond to standard treatment for SS and may suffer a prolonged and persistent course. (J Am Acad Dermatol 1999;40:838-41.) |
| Databáze: | OpenAIRE |
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