THE BASIC POINTS OF SAFE MANAGEMENT OF PREGNANCY AND DELIVERY IN PATIENTS WITH MARFAN SYNDROME
| Autor: | A. D. Makatsariya, D. V. Mitryuk, Viktoriya Bitsadze, L. S. Radetskaya, N. M. Khamani, N. A. Makatsariya |
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| Jazyk: | ruština |
| Rok vydání: | 2017 |
| Předmět: |
Marfan syndrome
Embryology medicine.medical_specialty inherited connective tissue disorders medicine.medical_treatment aortic dissection in pregnancy mesenchimal displasias Mitral valve medicine ehlers-danlos syndrome Caesarean section Aortic dissection Pregnancy Hysterectomy cesarean section business.industry Vaginal delivery Obstetrics and Gynecology Gynecology and obstetrics medicine.disease bleeding Surgery medicine.anatomical_structure Reproductive Medicine Ehlers–Danlos syndrome RG1-991 osler-weberrendu disease pregnancy hemorrhage business marfan syndrome |
| Zdroj: | Акушерство, гинекология и репродукция, Vol 11, Iss 3, Pp 82-87 (2017) |
| ISSN: | 2500-3194 2313-7347 |
| Popis: | Marfan syndrome is dominantly inherited connective tissue diseases, associated with microfibrillar fiber connective tissue deficiency in vascular walls, heart valves, joints, dural membrane, bones, and other organs. Diagnosis may be confirmed by clinical criteria and molecular tests. Pregnancy bears a risk of fatal complications, including aortic dissection, aortic root dilation, mitral valve insufficiency. Women must be followed and managed in a high risk pregnancy unit by a team from obstetricians, cardiologists, anesthetists, pediatricians, neonatologists and cardiac surgeons who are skilled in high risk pregnancies. This approach allows to avoid the serious maternal and fetal complications. Caesarean section should be offered for such patients, because it minimizes the hemodynamic changes, associated with vaginal delivery. Some authors recommend to perform post-cesarean hysterectomy, because of the high incidence of massive hemorrhage in postpartum. |
| Databáze: | OpenAIRE |
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