The Congenital Tricuspid Valve Spectrum: From Ebstein to Dysplasia
| Autor: | Naser M. Ammash, Joseph J. Maleszewski, Joseph A. Dearani, Muhammad Yasir Qureshi, Elizabeth H. Stephens |
|---|---|
| Rok vydání: | 2020 |
| Předmět: |
030204 cardiovascular system & hematology
03 medical and health sciences 0302 clinical medicine Humans Medicine cardiovascular diseases Cardiac Surgical Procedures Child Tricuspid valve business.industry General Medicine Anatomy medicine.disease Ebstein Anomaly medicine.anatomical_structure Congenital tricuspid regurgitation 030228 respiratory system EBSTEIN ANOMALY Echocardiography Dysplasia Pediatrics Perinatology and Child Health cardiovascular system Congenital tricuspid valve dysplasia Surgery Tricuspid Valve Cardiology and Cardiovascular Medicine business |
| Zdroj: | World Journal for Pediatric and Congenital Heart Surgery. 11:783-791 |
| ISSN: | 2150-136X 2150-1351 |
| DOI: | 10.1177/2150135120949235 |
| Popis: | Ebstein anomaly has a breadth of presentations, including “typical” and “atypical,” and can be confused with congenital tricuspid dysplasia. We summarize how to differentiate within this spectrum of disease. Both typical and atypical Ebstein have an underlying failure of delamination, but atypical Ebstein does not have ≥8mm/m2 apical septal leaflet displacement. In congenital tricuspid dysplasia, delamination is normal, while the leaflets and subvalvar apparatus are abnormal. To summarize, the sine qua non feature of Ebstein anomaly, present in both typical and atypical, is the failure of delamination. These are distinct from congenital tricuspid valve dysplasia in which the pathology is in the leaflet itself. |
| Databáze: | OpenAIRE |
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