Pulmonary venous hypertension may allow delayed palliation of single ventricle physiology with pulmonary hypertension
| Autor: | Raman Krishna Kumar, Gopalraj S. Sunil, Atul Kalantre |
|---|---|
| Rok vydání: | 2016 |
| Předmět: |
lcsh:Diseases of the circulatory (Cardiovascular) system
medicine.medical_specialty Hemodynamic Rounds lcsh:Medicine 030204 cardiovascular system & hematology hemodynamics 03 medical and health sciences single ventricle 0302 clinical medicine medicine.artery Internal medicine Medicine 030212 general & internal medicine Pulmonary wedge pressure Lung business.industry Vascular disease Delayed pulmonary artery banding lcsh:R lcsh:RJ1-570 lcsh:Pediatrics pulmonary venous hypertension (PVH) medicine.disease Pulmonary hypertension Surgery medicine.anatomical_structure lcsh:RC666-701 Ventricle Pediatrics Perinatology and Child Health Pulmonary artery Vascular resistance Cardiology Pulmonary venous hypertension Cardiology and Cardiovascular Medicine business |
| Zdroj: | Annals of Pediatric Cardiology, Vol 9, Iss 2, Pp 147-152 (2016) Annals of Pediatric Cardiology |
| ISSN: | 0974-2069 |
| DOI: | 10.4103/0974-2069.177517 |
| Popis: | Pulmonary vascular disease develops early in untreated single ventricle patients with increased pulmonary flow. Pulmonary artery (PA) banding is done at a young age in these patients in order to protect the lung vasculature and maintain low pulmonary artery pressures (PAP) and pulmonary vascular resistance (PVR). This also enables future completion of the single ventricle palliation. Pulmonary venous hypertension (PVH) secondary to left sided obstruction if present in addition in this setting contributes to the pulmonary arterial hypertension (PAH) but involves an element of reversibility of the PAH if the obstruction is relieved. We present two cases of single ventricle both of who re-presented late with PAH and PVH (secondary to mitral valve obstruction) and underwent delayed PA banding at 9.5 and 4.5 years of age respectively. Both patients however had different outcomes. The patient undergoing PA banding at 9.5 years successfully underwent a cavo-pulmonary shunt at the age of 12 years. The patient with PA banding at 4.5 years however, has residual PAH that presently precludes a cavo-pulmonary shunt. |
| Databáze: | OpenAIRE |
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