Gastrointestinal Behcet’s-like disease with myelodysplastic neoplasms with trisomy 8: a French case series and literature review
| Autor: | Julien Rossignol, Olivier Hermine, Salim Trad, Philippe Seksik, Arsène Mekinian, Lionel Ades, Alexis Guédon, N. Wesner, Jean Baptiste Fraison, Eric Liozon, Matthieu Ponsoye, Louis Drevon, Jerome Gillard, Olivier Fain, Pierre Fenaux, Benjamin Terrier, Jean Emmanuel Kahn, Achille Aouba, Fabrice Carrat, Kamel Laribi, Clement Gourguechon, Thomas Hanslik, Minhemon, On behalf Gfm |
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| Rok vydání: | 2018 |
| Předmět: |
Adult
Male Cancer Research medicine.medical_specialty Gastrointestinal Diseases Trisomy Behcet's disease Disease Trisomy 8 Diagnosis Differential 03 medical and health sciences 0302 clinical medicine medicine Humans Aged Aged 80 and over business.industry Behcet Syndrome food and beverages Hematology Middle Aged Prognosis medicine.disease Myelodysplastic-Myeloproliferative Diseases Dermatology eye diseases stomatognathic diseases Oncology Myelodysplastic Syndromes 030220 oncology & carcinogenesis Female business Chromosomes Human Pair 8 Follow-Up Studies 030215 immunology |
| Zdroj: | Leukemia & Lymphoma. 60:1782-1788 |
| ISSN: | 1029-2403 1042-8194 |
| DOI: | 10.1080/10428194.2018.1542152 |
| Popis: | We report the 11 cases of +8-MDS/MPN associated with Behcet's-like syndrome and compare them with Behcet's disease and Crohn's disease, pool with literature cases for analysis. Data for patients with +8-MDS/MPN and Behçet's-like syndrome were collected from MINHEMON. Eleven patients had Behcet's-like syndrome and +8-MDS/MPN (median age 75 years [IQR 65-87]; M/F ratio 0.8). MDS and Behcet's-like syndrome were diagnosed at the same time (7/11, 64%). By comparison with 63 patients with idiopathic Behcet's disease without associated MDS, those with Behcet's-like syndrome and +8-MDS/MPN were older (median 75 vs 48 years |
| Databáze: | OpenAIRE |
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