10.4021/jocmr2009.09.1264

Autor: Fereshteh rezakhanlu, Zhamak Khorgami, Nasim Sodagari, Shirzad Nasiri
Rok vydání: 2009
Předmět:
Zdroj: Journal of Clinical Medicine Research.
ISSN: 1918-3011
1918-3003
DOI: 10.4021/jocmr2009.09.1264
Popis: Malignant schwannoma of the anterior abdominal wall nerves is extremely rare. Malignant peripheral nerve sheath tumors (MPNST) represent approximately 10% of all soft tissue sarcomas and it is found in 4% of patients with neurofibromatosis 1. We present a case of malignant schwannoma in a 28-year-old female patient with neurofibromatosis 1. She presented with a painful mass in the right upper quadrant of her abdomen. The tumor location was in the abdominal wall in explorative laparatomy and malignant schwannoma was diagnosed in pathologic assessment. The tumor recurred in 3 months and computed tomography showed two masses in the right side of abdominopelvic cavity. Thereafter, second complete surgical resection was performed and pathologic finding was the same. In spite of administering chemotherapy after second surgery, the tumor recurred and magnetic resonance imaging finding showed a huge heterogeneously enhancing mass with adhesion to the inner side of the abdominal wall. The patient died because of acute respiratory failure due to multiple bilateral pulmonary metastases. Tumor location and rapid recurrence was unique in our patient. doi:10.4021/jocmr2009.09.1264
Databáze: OpenAIRE