Kardiomiopatia restrykcyjna – historia ze szczęśliwym zakończeniem
| Autor: | Beata Kierzkowska, Jerzy Stańczyk, Beata Chodór, Katarzyna Niewiadomska-Jarosik, Agata Zamecznik, Jarosław Rycaj |
|---|---|
| Rok vydání: | 2014 |
| Předmět: |
Heart transplantation
Constrictive pericarditis medicine.medical_specialty business.industry medicine.medical_treatment Diastole Restrictive cardiomyopathy medicine.disease Surgery Heart failure Internal medicine Pediatrics Perinatology and Child Health Ascites medicine Cardiology Differential diagnosis medicine.symptom business Cardiac catheterization |
| Zdroj: | Pediatria Polska. 89:285-291 |
| ISSN: | 0031-3939 |
| DOI: | 10.1016/j.pepo.2014.04.002 |
| Popis: | Cardiomyopathies are a group of rare diseases of a myocardium in a pediatric population which affect 1 – 1.5 cases per 100 000 children. Restrictive cardiomyopathy (RCM) is the least common type, which constitutes 2 – 5% of all cardiomyopathies. RCM is characterized by a diastolic dysfunction which is a result of an increased stiffness of the ventricular myocardium with a normal systolic function. Differential diagnosis should include especially constrictive pericarditis. Because of a poor prognosis, it is important to diagnose patients as soon as possible and to early qualify them for a heart transplantation. In this case report, we described the history of a 14-year-old boy with ascites, who was referred to the hospital with a suspicion of a liver failure. After performing detailed diagnostic tests (such as echocardiography, 24-hour ECG monitoring, magnetic resonance and cardiac catheterization), patient was initially diagnosed with idiopathic restrictive cardiomyopathy with QTc prolongation. As a result of pharmacotherapy (diuretics, anticoagulant doses of acetylsalicylic acid, β-blockers and magnesium) the general condition of the patient was stabilized. Six months after the final diagnosis heart transplantation was performed. |
| Databáze: | OpenAIRE |
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