Shone's syndrome: Insights from three-dimensional echocardiography
| Autor: | Martín Federico Vivas, Gustavo Avegliano, María Teresa Politi, Laura Mariana Riznyk, María F. Castro, Ricardo Ronderos |
|---|---|
| Rok vydání: | 2017 |
| Předmět: |
medicine.medical_specialty
business.industry Mitral ring Three dimensional echocardiography 030204 cardiovascular system & hematology medicine.disease Shone's syndrome Resection 03 medical and health sciences 0302 clinical medicine Mitral valve stenosis medicine.anatomical_structure 030228 respiratory system Internal medicine Mitral valve cardiovascular system medicine Cardiology Radiology Nuclear Medicine and imaging cardiovascular diseases Cardiology and Cardiovascular Medicine Subaortic stenosis business |
| Zdroj: | Echocardiography. 35:417-419 |
| ISSN: | 0742-2822 |
| DOI: | 10.1111/echo.13787 |
| Popis: | Shone's syndrome is a rare congenital anomaly defined as the presence of at least two of the following heart obstructions: a mitral supravalvular ring, a "parachute" mitral valve stenosis, subaortic stenosis, and aortic coarctation. A 58-year-old man presented with a mitral ring and a "parachute" mitral valve on two-dimensional transthoracic echocardiography, raising suspicion of Shone's syndrome. Three-dimensional transesophageal echocardiography revealed a subannular mitral ring inserted directly on the mitral leaflets, thus acting as a "valvar ring." This distinction can have therapeutic implications as a "valvar" mitral ring could require valve repair or replacement, instead of simple resection. |
| Databáze: | OpenAIRE |
| Externí odkaz: |
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