Anesthetic management of a pediatric patient with Loeys‐Dietz syndrome: A case report

Autor: Koui Ka, Yosuke Kamikado, Takahiro Mihara
Rok vydání: 2019
Předmět:
Zdroj: Pediatric Anesthesia. 29:875-877
ISSN: 1460-9592
1155-5645
DOI: 10.1111/pan.13673
Popis: Loeys-Dietz syndrome, a rare autosomal dominant disease, is characterized by arterial tortuosity and skeletal manifestations. We report anesthetic management of scoliosis surgery for a pediatric Loeys-Dietz syndrome patient. During surgery, severe hypotension occurred when a rotation-correction was performed; blood pressure returned to the baseline level after the maneuver was abandoned. We decided to not conduct rotation correction after discussing risks and benefits of the maneuver with surgeons. Since severe hemodynamic instability is expected in scoliosis surgery for Loeys-Dietz syndrome patients, we should be prepare for hemodynamic collapse and risks and benefits of the operative procedure should be discussed before undertaking the procedure.
Databáze: OpenAIRE
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