Malignant peripheral nerve sheath tumour of median nerve - an unusual presentation: a case report

Autor: Ramesh Vidyadharan, Danish Imran, Rajive Mathew Jose, Paul K. Wright, G. S. Rao
Rok vydání: 2005
Předmět:
Zdroj: European Journal of Plastic Surgery. 28:50-52
ISSN: 1435-0130
0930-343X
DOI: 10.1007/s00238-005-0751-1
Popis: Malignant peripheral nerve sheath tumours (MPNST) are rare tumours, which usually occur in patients with multiple neurofibromatosis. They are common in the head and neck and trunk and only a few cases have been reported in the hand. Many of these occur in patients with von Recklinghausen’s disease and rarely as a malignant transformation of benign schwannomas. When they appear in the hand they often present with various symptoms. We encountered a patient who presented with a longstanding asymptomatic swelling of the palm. On excision the histopathology showed a high-grade malignant peripheral nerve sheath tumour, which led us to speculate that a malignant transformation had occurred in a pre-existing benign swelling. This is reported for its unusual presentation, which, to our knowledge, has never been described previously.
Databáze: OpenAIRE